Giant Mesenchymal Hepatic Hamartomas With Adrenal Involvement Precipitating Respiratory Failure: A Myxomatous Mystery in a Three-Month-Old.

Authors

Ali Yasback, Nova Southeastern UniversityFollow
Abid Ulhaque, Trinity Medical Center
Tushar Chandra, Nemours Children's Hospital

Document Type

Article

Publication Date

4-12-2023

Publication Title

Cureus

Keywords

cysts, placental mesenchymal dysplasia, oncology, pediatric tumors, hepatic mesenchymal hamartoma

ISSN

2168-8184

Volume

15

Issue/No.

4

First Page

e37476

Abstract

The combination of placental mesenchymal dysplasia and hepatic mesenchymal hamartomas is an extremely rare finding. We present the case of a three-month-old female born at 35 weeks gestation with a history of placental mesenchymal dysplasia who presented with non-bilious, non-bloody emesis, and episodes of respiratory distress due to multiple enlarging abdominal cystic lesions. The patient's presentation was unique due to both liver and adrenal solid and cystic lesions. After extensive imaging and multiple biopsies, expert interpretation of biopsy tissue revealed hepatic mesenchymal hamartoma within the liver and the adrenal gland. To our knowledge, this is one of the few documented cases of unresectable hepatic mesenchymal hamartomas with adrenal involvement successfully undergoing a whole liver transplant.

Creative Commons License

This work is licensed under a Creative Commons Attribution 4.0 International License.

NSUWorks Citation

Yasback, Ali; Ulhaque, Abid; and Chandra, Tushar, "Giant Mesenchymal Hepatic Hamartomas With Adrenal Involvement Precipitating Respiratory Failure: A Myxomatous Mystery in a Three-Month-Old." (2023). HPD Articles. 404.
https://nsuworks.nova.edu/hpd_facarticles/404

DOI

10.7759/cureus.37476

Copyright

© Copyright 2023 Yasback et al.