Department of Audiology Faculty Articles

Title

Some Audiologic Characteristics in Individuals with Sotos Syndrome

ResearchID/ORCID ID

0000-0001-8330-9078, 0000-0001-6770-4377

ISBN or ISSN

2692-5877

Volume

3

Issue

5

Publication Date / Copyright Date

8-25-2020

First Page

1

Last Page

3

Publisher

IJCMCR

DOI Number

10.46998/IJCMCR.2020.03.000074

Abstract

We conducted an audiological assessment of 27 children and adults with Sotos syndrome in order to provide information about this population’s hearing and auditory processing abilities. Otoscopy, tympanometry, audiologic screening, distortion-product otoacoustic emissions (DPOAE) screening, speech-in-noise testing using the QuickSIN (SNR loss), and Dichotic Digits Test made up the test battery. Except for a small percentage of cases, otoscopy, tympanometry, and pure tone screening results were unremarkable and not unlike the general population. However, adults had large ear canal volumes similar to those reported in older adults in the general population. DPOAE screening was attempted with greater than expected referral rates, most likely due to cooperation issues and noise levels. SNR loss was generally higher (poorer) than published norms, and Dichotic Digit test results revealed a slight right ear advantage and an overall depression of scores in both ears compared to normative data. Results of the audiologic screenings indicated that the majority of individuals with Sotos syndrome do not appear to have hearing sensitivity issues co-occurring with the syndrome. However, QuickSIN and Dichotic Digit test results indicate that those with Sotos syndrome may have speech-in-noise and callosal-specific auditory transfer issues that together negatively impact complex listening.

Disciplines

Communication Sciences and Disorders | Medicine and Health Sciences | Speech and Hearing Science | Speech Pathology and Audiology

Keywords

auditory processing, hearing, Sotos syndrome

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